{"id":13208,"date":"2014-04-13T01:55:12","date_gmt":"2014-04-12T22:55:12","guid":{"rendered":"http:\/\/www.gncz.net\/behcet-hastaligi.html"},"modified":"2014-04-13T01:55:12","modified_gmt":"2014-04-12T22:55:12","slug":"behcet-hastaligi","status":"publish","type":"post","link":"https:\/\/gncz.net\/index.php\/behcet-hastaligi.html","title":{"rendered":"Beh\u00e7et Hastal\u0131\u011f\u0131"},"content":{"rendered":"\n<p>Prof.Dr. Hulusi Beh\u00e7et taraf\u0131ndan 1939 y\u0131l\u0131nda tan\u0131mlanm\u0131\u015ft\u0131r. Beh\u00e7et Hastal\u0131\u011f\u0131, a\u011f\u0131z i\u00e7i ve cinsel organ ve \u00e7evresinde yaralarla seyreden, ayr\u0131ca deri, g\u00f6z, orta ve b\u00fcy\u00fck eklemler, damarlar ba\u015fta olmak \u00fczere v\u00fccuttaki t\u00fcm organ ve dokular\u0131 tutabilen, nedeni belli olmayan bir hastal\u0131kt\u0131r.<\/p>\n<p> Beh\u00e7et Hastal\u0131\u011f\u0131n\u0131n hen\u00fcz belirlenmi\u015f bir nedeni yoktur. Ancak hastal\u0131\u011f\u0131 tetikleyen \u00e7evresel etkenlerin yan\u0131s\u0131ra mikrobik ajanlar, bakteri veya vir\u00fcsler ve genetik yatk\u0131nl\u0131k \u00fczerinde durulmaktad\u0131r. Ailesel ge\u00e7i\u015f hen\u00fcz tam bilinmemektedir. Ender olarak ailenin di\u011fer fertlerinde de g\u00f6r\u00fclebilmektedir.<\/p>\n<p>BEL\u0130RT\u0130LER\u0130 <\/p>\n<p> A\u011f\u0131z yaralar\u0131; A\u011f\u0131z yaralar\u0131 hastalar\u0131n hemen hemen hepsinde vard\u0131r.Hastal\u0131\u011f\u0131n di\u011fer belirtileri ortaya \u00e7\u0131kmadan y\u0131llarca \u00f6nce tek ba\u015f\u0131na g\u00f6r\u00fclebilir. Yaralar; yanak i\u00e7i, dil, dudaklar, yumu\u015fak damakta tek ya da \u00e7ok say\u0131da ortaya \u00e7\u0131kabilir. Yaralar\u0131n ortas\u0131 kirli beyaz, etraf\u0131 k\u0131zar\u0131k ve a\u011fr\u0131l\u0131d\u0131r. Genellikle 7 ile 14 G\u00fcn i\u00e7inde iyile\u015firler. Tekrarlay\u0131c\u0131 \u00f6zelliktedir ve tekrarlama s\u0131kl\u0131\u011f\u0131 hastadan hastaya de\u011fi\u015fir.<\/p>\n<p> Cinsel b\u00f6lge yaralar\u0131; Erkeklerde \u00e7o\u011funlukla torbalar (skrotum) \u00fczerinde, kad\u0131nlarda ise cinsel organ\u0131n b\u00fcy\u00fck ya da k\u00fc\u00e7\u00fck dudaklar\u0131 \u00fczerinde, \u00f6nce bir sivilce gibi ba\u015flar daha sonra a\u00e7\u0131k-oyuk ve a\u011fr\u0131l\u0131-ac\u0131l\u0131 bir yaraya d\u00f6n\u00fc\u015f\u00fcr. \u0130yile\u015fme s\u00fcresi 14 G\u00fcne kadar uzayabilir, ve bir seferde birden fazla yara a\u00e7\u0131labilir. \u0130yile\u015fti\u011fi yerde genellikle iz b\u0131rak\u0131r.<\/p>\n<p> \u00c7e\u015fitli Deri Belirtileri; Beh\u00e7et hastal\u0131\u011f\u0131nda deriye ait belirtiler, hastal\u0131\u011f\u0131n ba\u015flang\u0131c\u0131nda veya seyri esnas\u0131nda s\u0131k g\u00f6r\u00fcl\u00fcr. Genelde bacaklar\u0131n \u00f6n y\u00fcz\u00fcnde k\u0131rm\u0131z\u0131 ve a\u011fr\u0131l\u0131 d\u00fc\u011fme gibi sertlikler g\u00f6r\u00fcl\u00fcr. Bunlar nadiren de g\u00f6vdede d\u00fczensiz ve da\u011f\u0131n\u0131k olarak yerle\u015firler. \u00c7aplar\u0131 1-5 santimetre aras\u0131ndad\u0131r. 10-15 g\u00fcn i\u00e7inde, ba\u015f vermeden ve a\u00e7\u0131k yara haline d\u00f6nmeden, kimi zaman yerlerinde hafif bir leke b\u0131rakarak iyile\u015firler. Sivilce benzeri belirtiler,ba\u015f veren iltihapl\u0131 kabarc\u0131klard\u0131r. G\u00f6r\u00fcn\u00fcm a\u00e7\u0131s\u0131ndan sivilce ya da \u00e7\u0131bandan farkl\u0131 de\u011fildir. Bu nedenle hastal\u0131\u011f\u0131n di\u011fer belirtileri ile birlikte de\u011ferlendirmek gerekir. S\u0131rt, y\u00fcz, g\u00f6\u011f\u00fcs, kas\u0131klar, kal\u00e7alar, cinsel b\u00f6lge, kol ve bacaklarda ortaya \u00e7\u0131karlar. V\u00fccudun genellikle koltuk alt\u0131, meme, Ayak parmak aralar\u0131 ve cinsel b\u00f6lge haricinde, a\u011f\u0131z i\u00e7indeki aftlara benzeyen yaralar g\u00f6r\u00fclebilir. Bunlar di\u011fer belirtilerine g\u00f6re daha az ortaya \u00e7\u0131kar.<\/p>\n<p> G\u00f6z ile ilgili belirtiler; S\u0131kl\u0131\u011f\u0131 ve \u015fiddeti de\u011fi\u015fkenlik g\u00f6steren g\u00f6z tutulmas\u0131; gen\u00e7 erkeklerde daha s\u0131k, kad\u0131nlarda ve ya\u015fl\u0131larda daha seyrek ve hafiftir. Hastalar\u0131n ba\u015fl\u0131ca \u015fikayeti g\u00f6z \u00f6n\u00fcnde bir t\u00fcl varm\u0131\u015f gibi bulan\u0131k g\u00f6rme, g\u00f6z \u00e7evresinde a\u011fr\u0131, kanlanma, g\u00f6z\u00fcn \u0131\u015f\u0131ktan rahats\u0131z olmas\u0131, puslanma, perdelenme ve siyah nokta u\u00e7u\u015fmalar\u0131d\u0131r.<\/p>\n<p> Eklem Belirtileri; Beh\u00e7et hastalar\u0131nda s\u0131kl\u0131kla b\u00fcy\u00fck eklemler; diz, ayak bile\u011fi, el bile\u011fi ve dirsek tutulur. Ayr\u0131ca el ve ayak eklemlerinde, parmak eklemlerinde ve kal\u00e7a eklemlerinde Beh\u00e7et Hastal\u0131\u011f\u0131na ba\u011fl\u0131 belirtiler olabilir. Eklem tutulmas\u0131 eklem a\u011fr\u0131s\u0131 ve eklem \u015fi\u015fmesi \u015feklinde ortaya \u00e7\u0131kar. Eklemde hareket k\u0131s\u0131tl\u0131l\u0131\u011f\u0131 g\u00f6r\u00fcl\u00fcrken k\u0131zar\u0131kl\u0131\u011fa pek rastlanmaz. Eklem tutulumu \u015fekil bozuklu\u011fu yapmaz ve genellikle de 1-2 hafta i\u00e7inde kendili\u011finden iyile\u015fir.<\/p>\n<p> Damar belirtileri; Beh\u00e7et hastal\u0131\u011f\u0131nda hem atardamar hem de toplardamarlar hastalanabilir. Y\u00fczeyel toplardamar tutulmas\u0131 bacakta ip gibi uzayan veya yuvarlak \u015fi\u015flik, k\u0131zar\u0131kl\u0131k, a\u011fr\u0131 \u015feklinde kendini g\u00f6sterir. B\u00fcy\u00fck toplardamarlar\u0131n tutulmas\u0131 halinde bir bacakta dizden a\u015fa\u011f\u0131 do\u011fru \u015fi\u015fme ortaya \u00e7\u0131kabilir.<\/p>\n<p> Sinir Sistemi Belirtileri; Sinir sistemi tutulumu \u00e7ok nadir g\u00f6r\u00fcl\u00fcr. Hastalarda ara-ara ortaya \u00e7\u0131kan \u00e7ift g\u00f6rme, kol veya bacaklarda uyu\u015fukluk, kuvvetsizlik, denge bozuklu\u011fu, y\u00fcr\u00fcme zorlu\u011fu, konu\u015fma bozuklu\u011fu, unutkanl\u0131k gibi belirtiler olabilir.<\/p>\n<p> Mide-Barsak Belirtileri; Hastalarda ender olarak bo\u011faz a\u011fr\u0131s\u0131, kar\u0131n a\u011fr\u0131s\u0131, ishal, i\u015ftahs\u0131zl\u0131k, bulant\u0131, kab\u0131zl\u0131k g\u00f6r\u00fclebilir.<\/p>\n<p> Akci\u011fer Belirtileri; Beh\u00e7et Hastal\u0131\u011f\u0131 nadiren akci\u011ferin ana atar damar\u0131nda balonla\u015fmaya neden olabilir. Bu durumda hastalarda kanl\u0131 balgam yak\u0131nmalar\u0131 ortaya \u00e7\u0131kar.<\/p>\n<p> Beh\u00e7et hastal\u0131\u011f\u0131n\u0131n belirtileri; Beh\u00e7et hastal\u0131\u011f\u0131 genel anlamda bir damar iltihab\u0131d\u0131r denebilir. Belirtilerin t\u00fcm\u00fcn\u00fcn ayn\u0131 anda ortaya \u00e7\u0131kmas\u0131 \u015fart de\u011fildir. Baz\u0131 belirtiler hastal\u0131\u011f\u0131n ilk y\u0131llar\u0131nda yok iken daha sonraki y\u0131llarda ortaya \u00e7\u0131kabilir.<\/p>\n<p> TANI<\/p>\n<p> Beh\u00e7et hastal\u0131\u011f\u0131 tan\u0131s\u0131n\u0131n konulabilmesi i\u00e7in a\u011f\u0131z aftlar\u0131n\u0131n olmas\u0131 \u015fartt\u0131r. A\u011f\u0131z yaralar\u0131 (oral aft) ile birlikte cinsel b\u00f6lge yaralar\u0131, g\u00f6z bulgular\u0131, deride k\u0131rm\u0131z\u0131 sertlikler, k\u0131l dibi iltihaplar\u0131 ve Pozitif paterji testinin varl\u0131\u011f\u0131 gibi bulgular\u0131n birka\u00e7\u0131n\u0131n bulunmas\u0131 te\u015fhis i\u00e7in gereklidir. Paterji testi Beh\u00e7et hastal\u0131\u011f\u0131 tan\u0131s\u0131na yard\u0131mc\u0131 olmak \u00fczere uygulanan bir cilt testidir, hastan\u0131n \u00f6nkol derisine steril bir i\u011fne bat\u0131r\u0131larak yap\u0131l\u0131r. Reaksiyon 24 Saatte belirginle\u015fip 48 saatte maksimum seviyeye ula\u015f\u0131r. \u00d6nce k\u0131rm\u0131z\u0131 1-2 milimetrelik bir kabar\u0131kl\u0131k iken iltihapl\u0131 sivilce haline de d\u00f6nebilir. Paterji testinin pozitif olmas\u0131 Beh\u00e7et hastalar\u0131nda tan\u0131 kriteri olarak kabul edilir.<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Tedavinin se\u00e7imi hastan\u0131n klinik belirtilerine ba\u011fl\u0131d\u0131r. Alevlenmeler ve d\u00fczelmelerle seyreden bu hastal\u0131k zaman i\u00e7inde belirtilerinin hafifledi\u011fi veya kayboldu\u011fu devreler g\u00f6sterebilir. Tedavi lokal (yerel, b\u00f6lgesel) ve sistemik olmak \u00fczere iki k\u0131s\u0131mdan olu\u015fur. Lokal tedavi deri, a\u011f\u0131z i\u00e7i ve cinsel b\u00f6lge belirtilerinde uygulan\u0131r. Sistemik tedavi ise organ tutulumlar\u0131nda kullan\u0131l\u0131r.<\/p>\n<p>HAZIRLAYANLAR; Dr Sevtap \u015e\u0130M\u015eEK, Prof Dr Ya\u015far KARAASLAN<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Prof.Dr. Hulusi Beh\u00e7et taraf\u0131ndan 1939 y\u0131l\u0131nda tan\u0131mlanm\u0131\u015ft\u0131r. Beh\u00e7et Hastal\u0131\u011f\u0131, a\u011f\u0131z i\u00e7i ve cinsel organ ve \u00e7evresinde yaralarla seyreden, ayr\u0131ca deri, g\u00f6z, orta ve b\u00fcy\u00fck eklemler, damarlar ba\u015fta olmak \u00fczere v\u00fccuttaki t\u00fcm organ ve dokular\u0131 tutabilen, nedeni belli olmayan bir hastal\u0131kt\u0131r. Beh\u00e7et Hastal\u0131\u011f\u0131n\u0131n hen\u00fcz belirlenmi\u015f bir nedeni yoktur. Ancak hastal\u0131\u011f\u0131 tetikleyen \u00e7evresel etkenlerin yan\u0131s\u0131ra mikrobik ajanlar, bakteri veya vir\u00fcsler ve genetik<a class=\"more-link\" href=\"https:\/\/gncz.net\/index.php\/behcet-hastaligi.html\">[Devam\u0131n\u0131 Oku&#8230;]<\/a><\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":[],"categories":[22524],"tags":[23099,23102,23106,23104,23107,23105,23097],"_links":{"self":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/posts\/13208"}],"collection":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/comments?post=13208"}],"version-history":[{"count":0,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/posts\/13208\/revisions"}],"wp:attachment":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/media?parent=13208"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/categories?post=13208"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/tags?post=13208"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}