{"id":13275,"date":"2014-04-13T01:58:12","date_gmt":"2014-04-12T22:58:12","guid":{"rendered":"http:\/\/www.gncz.net\/akcigerin-dogumsal-hastaliklari.html"},"modified":"2014-04-13T01:58:12","modified_gmt":"2014-04-12T22:58:12","slug":"akcigerin-dogumsal-hastaliklari","status":"publish","type":"post","link":"https:\/\/gncz.net\/index.php\/akcigerin-dogumsal-hastaliklari.html","title":{"rendered":"Akci\u011ferin Do\u011fumsal Hastal\u0131klar\u0131"},"content":{"rendered":"\n<p>Akci\u011ferin do\u011fumsal hastal\u0131klar\u0131n\u0131n \u00e7o\u011fu yeni do\u011fan veya bebeklik d\u00f6neminde ortaya \u00e7\u0131kan solunum \u015fikayetleri ile birlikte fark edilir. Hamilelik s\u0131ras\u0131nda tan\u0131 konulma oran\u0131 y\u00fcksektir.TRAKEA AGENEZ\u0130 ve ATREZ\u0130 <\/p>\n<p> Do\u011fumla birlikte solunum yetmezli\u011fi g\u00f6r\u00fcl\u00fcr ve \u00e7o\u011funlukla \u00f6l\u00fcmc\u00fcld\u00fcr.<\/p>\n<p> TANI<\/p>\n<p> Do\u011fumda bebekler mavi renkte cilde sahiptirler ve a\u011flamazlar. \u00c7o\u011funlukla beraberinde kalp, omurga veya bat\u0131nla ilgili anormallikleri de vard\u0131r.<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Yeni bir soluk borusu olu\u015fturmay\u0131 sa\u011flamak amac\u0131yla yap\u0131lacak cerrahidir.<\/p>\n<p>BRON\u015e\u0130AL ANORMALL\u0130KLER <\/p>\n<p> 1- Trakeal Divertikulum <\/p>\n<p> Soluk borusunun \u00fcst k\u0131s\u0131mlar\u0131ndan kaynaklanan, k\u00f6r olarak sonlanan veya geli\u015fmemi\u015f akci\u011fer dokusuna a\u00e7\u0131lan bir kanald\u0131r.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> B\u00fcy\u00fcyerek kom\u015fu organlara bas\u0131 yapabilir veya tekrarlayan uzun s\u00fcreli akci\u011fer enfeksiyonlara sebep olabilir.<\/p>\n<p> TANI<\/p>\n<p> Bilgisayarl\u0131 Tomografi ve Bronkoskopi (akci\u011fer sisteminin Alet yard\u0131m\u0131yla g\u00f6zle izlenmesi)<\/p>\n<p> TEDAV\u0130S\u0130<\/p>\n<p> Bu kanal\u0131n cerrahi olarak \u00e7\u0131kar\u0131lmas\u0131d\u0131r<\/p>\n<p>2- Trakeal Bronkus: <\/p>\n<p> normal akci\u011fer dokusuna giden soluk borusu par\u00e7as\u0131n\u0131n (bron\u015f) normalden daha \u00fcst seviyelerden \u00e7\u0131kmas\u0131d\u0131r.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> Bu par\u00e7an\u0131n t\u0131kanmas\u0131 veya birlikte olan ek anormalliklerine ba\u011fl\u0131 \u015fikayetler ve zat\u00fcrre, solunum yetmezli\u011fi g\u00f6r\u00fclebilir.<\/p>\n<p> TANI<\/p>\n<p> Bilgisayarl\u0131 Tomografi, Bronkoskopi<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Anormal soluk borusu kanal\u0131n\u0131n cerrahi olarak \u00e7\u0131kart\u0131lmas\u0131d\u0131r.<\/p>\n<p>3- Bron\u015fial Atrezi <\/p>\n<p> Akci\u011fer dokusunda k\u00f6r olarak sonlanan bron\u015f par\u00e7as\u0131d\u0131r. Do\u011fumda etkilenen akci\u011fer b\u00f6lgesi S\u0131v\u0131 ile dolu oldu\u011fundan saydam olarak g\u00f6zlenir.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> Isl\u0131k \u00e7alar gibi nefes al\u0131rlar. Akci\u011fer enfeksiyonu riski fazlad\u0131r.<\/p>\n<p> TANI<\/p>\n<p> Bilgisayarl\u0131 Tomografi<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Cerrahi olarak hastal\u0131kl\u0131 k\u0131sm\u0131n \u00e7\u0131kar\u0131lmas\u0131 yeterlidir.<\/p>\n<p>4- Trakea\u00f6zafagial f\u0131st\u00fcl <\/p>\n<p> Soluk borusu ile yemek borusu aras\u0131nda do\u011fumsal olarak ba\u011flant\u0131 bulunmas\u0131d\u0131r.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> Hastalarda solunum s\u0131k\u0131nt\u0131s\u0131 ve zat\u00fcrre mevcuttur.<\/p>\n<p> TANI<\/p>\n<p> Yemek borusunun ila\u00e7l\u0131 filminin \u00e7ekilmesi<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Aradaki ba\u011flant\u0131n\u0131n cerrahi olarak \u00e7\u0131kart\u0131lmas\u0131 gereklidir<\/p>\n<p>5- Bron\u015fial Stenoz<\/p>\n<p> Akci\u011fere giden bron\u015flar\u0131n darl\u0131\u011f\u0131d\u0131r. Akci\u011fere Hava girer fakat \u00e7\u0131kmas\u0131 zordur.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> Hastalarda kronik akci\u011fer enfeksiyonu g\u00f6r\u00fcl\u00fcr.<\/p>\n<p> TANI<\/p>\n<p> Bronkoskopi<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Daralm\u0131\u015f bron\u015f k\u0131sm\u0131n\u0131n geni\u015fletilmesi<\/p>\n<p>KONJEN\u0130TAL LOBER AMF\u0130ZEM <\/p>\n<p> Akci\u011ferin bir par\u00e7as\u0131n\u0131n a\u015f\u0131r\u0131 hava ile dolmas\u0131d\u0131r.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> \u00c7ocukluk \u00e7a\u011f\u0131nda \u015fikayetler g\u00f6r\u00fclmeye ba\u015flar. Do\u011fumla birlikte h\u0131zl\u0131 nefes al\u0131p verme, g\u00f6\u011f\u00fcs duvar\u0131nda nefes almakla birlikte olu\u015fan \u00e7ekintiler ve \u0131sl\u0131k \u00e7alar \u015fekilde soluk al\u0131p verme vard\u0131r. S\u0131k \u00fcst solunum yollar\u0131 enfeksiyonu ge\u00e7irirler.<\/p>\n<p> TANI<\/p>\n<p> Etkilenen k\u0131s\u0131mda akci\u011fer sesleri azalm\u0131\u015ft\u0131r. Akci\u011fer grafilerinde etkilenen k\u0131s\u0131m normal b\u00f6lgelere g\u00f6re daha siyah renkte oldu\u011fu g\u00f6zlenir. Bilgisayarl\u0131 tomografi tan\u0131da faydal\u0131d\u0131r.<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Etkilenen akci\u011fer k\u0131sm\u0131n\u0131n cerrahi olarak \u00e7\u0131kar\u0131lmas\u0131 gerekir.<\/p>\n<p>PULMONER AGENEZ\u0130(TEK TARAFLI AKC\u0130\u011eER\u0130N YOKLU\u011eU) <\/p>\n<p> Tek tarafl\u0131 Akci\u011fer tomurcu\u011funun yoklu\u011fu sonucu akci\u011fer dokusunun ve damarlar\u0131n\u0131n olu\u015fmamas\u0131d\u0131r. Beraberinde kalp hastal\u0131klar\u0131 ve kromozom anormallikleri de g\u00f6r\u00fclebilir.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> Yeni do\u011fan d\u00f6neminde nefes darl\u0131\u011f\u0131, s\u0131k nefes al\u0131p verme ve morarma g\u00f6zlenebilir. Daha b\u00fcy\u00fck \u00e7ocuklarda nefes al\u0131p verirken \u0131sl\u0131k sesine benzer ses duyulur.<\/p>\n<p> TANI<\/p>\n<p> G\u00f6\u011f\u00fcs kafesi d\u0131\u015ftan normal g\u00f6r\u00fcn\u00fcr. Fakat kalp ve g\u00f6\u011f\u00fcs i\u00e7i organlar etkilenen tarafa do\u011fru \u00e7ekilmi\u015ftir.<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Tedavi gerekli de\u011fildir, ek kalp hastal\u0131\u011f\u0131 varsa bunlar\u0131n tedavisi yeterlidir. <\/p>\n<p>PULMONER H\u0130POPLAZ\u0130(AKC\u0130\u011eERLER\u0130N YETERS\u0130Z GEL\u0130\u015e\u0130M\u0130) <\/p>\n<p> Akci\u011ferleri olu\u015fturan alveollerin say\u0131 ve a\u011f\u0131rl\u0131k olarak azl\u0131\u011f\u0131 mevcuttur.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> Do\u011fumdan sonra \u015fikayetler ba\u015flar. \u015eiddetli solunum yetmezli\u011fi g\u00f6r\u00fcl\u00fcr.<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Oksijen deste\u011fi<\/p>\n<p>SEKESTRASYON <\/p>\n<p> Normal solunum yollar\u0131 ile ba\u011flant\u0131s\u0131 olmayan akci\u011fer dokusuna denir. Ayr\u0131ca damarsal beslenmesini kalp yerine kalpten \u00e7\u0131kan b\u00fcy\u00fck damarlardan al\u0131r. \u0130ki tipi vard\u0131r. Ya normal akci\u011fer dokusundan ayr\u0131lm\u0131\u015f haldedir ya da normal akci\u011fer dokusunun i\u00e7inde geli\u015fir.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> S\u0131k tekrarlayan akci\u011fer enfeksiyonlar\u0131 g\u00f6r\u00fcl\u00fcr.<\/p>\n<p> TANI<\/p>\n<p> Hamilelikte anne karn\u0131nda Ultrasonografi ile tan\u0131 konabilir. Do\u011fumdan sonra ise bilgisayarl\u0131 tomografi tan\u0131 koymada faydal\u0131d\u0131r.<\/p>\n<p> TEDAV\u0130<\/p>\n<p> Hastal\u0131kl\u0131 akci\u011fer par\u00e7as\u0131n\u0131n cerrahi olarak \u00e7\u0131kar\u0131lmas\u0131 yeterlidir. <\/p>\n<p>BRONKOJEN\u0130K K\u0130ST <\/p>\n<p> Akci\u011ferlerin i\u00e7inde veya kom\u015fu b\u00f6lgelerinde olu\u015fan do\u011fumsal kistleri tarif eder. \u00c7o\u011funlukla tektir fakat birden fazlada olabilir.<\/p>\n<p> BEL\u0130RT\u0130LER<\/p>\n<p> \u00c7o\u011funlukla \u015fikayet yoktur. Kist i\u00e7eri\u011fi patlarsa enfeksiyon \u015fikayetleri verebilir. TANI<\/p>\n<p> Hamilelik esnas\u0131nda ultrasonografi ile tan\u0131 konabilir. Do\u011fumdan sonra ise Bilgisayarl\u0131 tomografi tan\u0131da faydal\u0131d\u0131r.<\/p>\n<p> TEDAV\u0130: Kistin tek ba\u015f\u0131na \u00e7\u0131kar\u0131lmas\u0131 tedavi i\u00e7in yeterlidir. <\/p>\n<p>KORUNMA <\/p>\n<p> Yak\u0131n akraba evliliklerinden sak\u0131n\u0131n\u0131z. Hamilelik esnas\u0131nda Utrasonografi kontrollerinizi aksatmay\u0131n\u0131z <\/p>\n<p>HAZIRLAYAN: Do\u00e7. Dr Yurdanur ERDO\u011eAN<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Akci\u011ferin do\u011fumsal hastal\u0131klar\u0131n\u0131n \u00e7o\u011fu yeni do\u011fan veya bebeklik d\u00f6neminde ortaya \u00e7\u0131kan solunum \u015fikayetleri ile birlikte fark edilir. Hamilelik s\u0131ras\u0131nda tan\u0131 konulma oran\u0131 y\u00fcksektir.TRAKEA AGENEZ\u0130 ve ATREZ\u0130 Do\u011fumla birlikte solunum yetmezli\u011fi g\u00f6r\u00fcl\u00fcr ve \u00e7o\u011funlukla \u00f6l\u00fcmc\u00fcld\u00fcr. TANI Do\u011fumda bebekler mavi renkte cilde sahiptirler ve a\u011flamazlar. \u00c7o\u011funlukla beraberinde kalp, omurga veya bat\u0131nla ilgili anormallikleri de vard\u0131r. TEDAV\u0130 Yeni bir soluk borusu olu\u015fturmay\u0131 sa\u011flamak<a class=\"more-link\" href=\"https:\/\/gncz.net\/index.php\/akcigerin-dogumsal-hastaliklari.html\">[Devam\u0131n\u0131 Oku&#8230;]<\/a><\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":[],"categories":[22524],"tags":[23283],"_links":{"self":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/posts\/13275"}],"collection":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/comments?post=13275"}],"version-history":[{"count":0,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/posts\/13275\/revisions"}],"wp:attachment":[{"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/media?parent=13275"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/categories?post=13275"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/gncz.net\/index.php\/wp-json\/wp\/v2\/tags?post=13275"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}